Eosinophilic polyangiitis with granulomatosis

    • Eosinophilic Granulomatosis with Polyangiitis: A Systematic …

      https://acrjournals.onlinelibrary.wiley.com/doi/epdf/10.1002/acr2.11194

      Eosinophilic granulomatosis with polyangiitis (EGPA) is part of a group of vasculitides commonly referred to as antineutrophil cytoplasmic antibody (ANCA)–associated vasculitis (AAV), in addition to granulomatosis with polyangiitis (GPA), microscopic polyangiitis (MPA), and renal-limited vasculitis. Patients with EGPA characteristically have ...

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    • [PDF File] Benralizumab as a Steroid-Sparing Treatment Option in …

      https://www.researchgate.net/profile/Vamsi-Guntur-2/publication/346205964_Benralizumab_as_a_Steroid-Sparing_Treatment_Option_in_Eosinophilic_Granulomatosis_with_Polyangiitis/links/6213e5166c472329dcfb8661/Benralizumab-as-a-Steroid-Sparing-Treatment-Option-in-Eosinophilic-Granulomatosis-with-Polyangiitis.pdf

      Eosinophilic granulomatosis with polyangiitis (EGPA), pre-viously known as Churg-Strauss syndrome, is a hypereosinophilic disorder characterized by asthma, blood eosinophilia, chronic

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    • Mepolizumab for Eosinophilic Granulomatosis With …

      https://acrjournals.onlinelibrary.wiley.com/doi/epdf/10.1002/art.41943

      Eosinophilic granulomatosis with polyangiitis (EGPA) is an antineutrophil cytoplasmic antibody (ANCA)–associated vasculitis characterized by asthma, ear, nose, and throat (ENT) involve-ment, blood and tissue eosinophilia, and systemic vasculitis manifestations (1,2). Treatment mainly relies on systemic gluco-

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    • [PDF File] Case Report Open Access A Case Report of Eosinophilic …

      https://www.onlinescientificresearch.com/articles/a-case-report-of-eosinophilic-granulomatosis-with-polyangiitis-in-a-pediatric-patient.pdf

      Introduction: Eosinophilic Granulomatosis with polyangiitis (EGPA), formerly known as Churg-Strauss syndrome (CSS), is a rare systemic vasculitis of small and medium-sized vessels that primarily develops in middle-aged individuals. It is characterized by asthma, blood eosinophilia, and extrapulmonary manifestations.

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    • [PDF File] Burden of illness associated with eosinophilic …

      https://link.springer.com/content/pdf/10.1007/s10067-021-05783-8.pdf

      Eosinophilic granulomatosis with polyangiitis (EGPA) is a rare disease associated with vascular inflammation and multisys - tem organ damage. The literature reporting EGPA incidence or prevalence is limited. We performed a systematic literature review and meta-analysis to describe the incidence, prevalence, and disease burden associated with EGPA.

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    • Eosinophilic granulomatosis with polyangiitis (Churg …

      https://onlinelibrary.wiley.com/doi/pdfdirect/10.1111/all.12088

      REVIEW ARTICLE Eosinophilic granulomatosis with polyangiitis (Churg–Strauss): state of the art A. Vaglio1, C. Buzio1 & J. Zwerina2,3 1Department of Clinical Medicine, Nephrology and Health Sciences, University Hospital of Parma, Parma, Italy; 2Department of Internal Medicine 3, Institute for Clinical Immunology, University of Erlangen-Nuremberg, …

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    • [PDF File] Eosinophilic Granulomatosis with Polyangiitis and Atopy:

      https://www.researchgate.net/publication/348846441_Eosinophilic_Granulomatosis_with_Polyangiitis_and_Atopy_A_Case_Report/fulltext/6012f137a6fdcc071b9cf414/Eosinophilic-Granulomatosis-with-Polyangiitis-and-Atopy-A-Case-Report.pdf

      Case report. We report the case of a 36-year-old male who was diagnosed dur-ing the first months of his life with AE and subsequently with an allergy to egg-white proteins. When he was a teenager ...

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    • [PDF File] Eosinophilic Granulomatosis With Polyangiitis (Churg …

      http://5y1.org/file/8050/eosinophilic-granulomatosis-with-polyangiitis-churg.pdf

      Eosinophilic granulomatosis with polyangiitis (Churg-Strauss) (EGPA) is one of the rarest but still potentially life-threatening systemic necrotizing vascu-litides predominantly affecting small vessels (1–3). Since the first description of the disease in 1951 (4), several descriptive series have been published, but each in-

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    • [PDF File] Adding Azathioprine to Remission‐Induction Glucocorticoids …

      http://5y1.org/file/8050/adding-azathioprine-to-remission‐induction-glucocorticoids.pdf

      nonsevere eosinophilic granulomatosis with polyangiitis (Churg-Strauss) (EGPA), microscopic polyangiitis (MPA), or polyarteritis nodosa (PAN). Methods. All patients included in this double-blind trial received glucocorticoids, gradually tapered ClinicalTrials.gov identifier: NCT00647166. over 12 months, and were randomized to …

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    • [PDF File] Eosinophilic Granulomatosis With Polyangiitis: Dissecting …

      https://www.researchgate.net/publication/349556755_Eosinophilic_Granulomatosis_With_Polyangiitis_Dissecting_the_Pathophysiology/fulltext/6050deefa6fdccbfeae5f094/Eosinophilic-Granulomatosis-With-Polyangiitis-Dissecting-the-Pathophysiology.pdf

      Eosinophilic Granulomatosis with Polyangiitis (EGPA) is a rare multisystemic disease classified both amongst hypereosinophilic disorders and ANCA-associated vasculitis. Vessel inflammation and ...

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    • [PDF File] Eosinophilic Granulomatosis with Polyangiitis - IMJ

      https://imj.ie/wp-content/uploads/2021/12/Eosinophilic-Granulomatosis-with-Polyangiitis.pdf

      known as Eosinophilic granulomatosis with polyangiitis (EGPA) in 2012, in keeping with new nomenclature. EGPA is a multisystem disorder characterised by necrotizing small and medium vessel vasculitis1. Its annual incidence is low with 0.5 – 4.2 cases per million3 and usually arises in people aged 40 to

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    • [PDF File] 2022 American College of Rheumatology/European Alliance

      https://www.feinberg.northwestern.edu/sites/firstdailylife/docs/Eosinophilic_Granulomatosis_with_Polyangiitis.pdf

      Eosinophilic Granulomatosis With Polyangiitis Peter C. Grayson,1 Cristina Ponte,2 Ravi Suppiah,3 Joanna C. Robson,4 Anthea Craven,5 Andrew Judge,6 Sara Khalid,5 Andrew Hutchings,7 Raashid A. Luqmani,5 Richard A. Watts,8 and Peter A Merkel9 Objective. To develop and validate revised classification criteria for eosinophilic granulomatosis with ...

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    • Eosinophilic granulomatosis with polyangiitis after …

      https://www.jaci-global.org/article/S2772-8293(22)00032-7/pdf

      Eosinophilic granulomatosis with polyangiitis (EGPA) is a type of systemic vasculitis that develops following prodromes such as asthma, chronic rhinosinusitis with nasal polyps (CRSwNP), and hypereosinophilia. More than half of the cases are antineutrophil cytoplasmic antibody (ANCA)-negative, and these cases may have genetic backgrounds ...

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    • [PDF File] Eosinophilic granulomatosis with polyangiitis (Churg …

      http://5y1.org/file/8050/eosinophilic-granulomatosis-with-polyangiitis-churg.pdf

      REVIEW ARTICLE Eosinophilic granulomatosis with polyangiitis (Churg–Strauss): state of the art A. Vaglio1, C. Buzio1 & J. Zwerina2,3 1Department of Clinical Medicine, Nephrology and Health Sciences, University Hospital of Parma, Parma, Italy; 2Department of Internal Medicine 3, Institute for Clinical Immunology, University of Erlangen-Nuremberg, …

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