ࡱ>  hj[\]^_`abcdefg p+bjbj `rr  <<IIIIIT>J>J>JJK>J[FO U6U6U6UWr'\][[[[[[[$z_,bC[]I^uW@W^^C[II6U6U?[yyy^.I6UI6U[y^[yy NZ6Up?X'dJT [[0[YbjT bXZZbIZ`y^^^C[C[kt^^^[^^^^b^^^^^^^^^< H:  Ashford and St. Peters Hospitals NHS Foundation Trust Neonatal Intensive Care Unit The Postnatal Ward Handbook:  HYPERLINK \l "duties"Duties and responsibilities of the junior doctors  HYPERLINK \l "Routine"The Routine examination of the newborn  HYPERLINK \l "Commonly"Commonly encountered problems:  HYPERLINK \l "Cardiovascular"Cardiovascular system  HYPERLINK \l "Respiratory"Respiratory system  HYPERLINK \l "Neurological"Neurological system  HYPERLINK \l "Gastrointestinal"Gastrointestinal system  HYPERLINK \l "Musculoskeletal"Musculoskeletal system / Orthopaedics  HYPERLINK \l "Renal"Renal system  HYPERLINK \l "Genitalia"Genitalia  HYPERLINK \l "Eyes"Eyes  HYPERLINK \l "Infections"Infections / BCG and other vaccinations  HYPERLINK \l "Feeding"Feeding / Palate  HYPERLINK \l "Physiotherapy"Physiotherapy F/U  HYPERLINK \l "Audiology"Audiology  HYPERLINK \l "Syndromes"Syndromes  HYPERLINK \l "Others"Others Please note: The clinical guideline links in this handbook are correct as at the publication date. If a link is broken, this document will need to be updated accordingly. The full list of neonatal guidelines can be found on the trust intranet. Duties and responsibilities of the junior doctors There are 3 postnatal ward SHOs one for Special Care Unit and two for Joan Booker Ward and you will all work together as a team. The GP trainees and the FY2s from General Paediatrics are mainly allocated to do the baby checks (Baby check SHO). The NICU SHOs are mainly responsible for seeing any babies that need a paediatric review (Neonatal Reviews SHO). The NICU SHO will help and support the Baby Check SHO, once all babies that require bloods or a management plan are seen. This role allocation does not mean that there is no cross-over of responsibilities. The GP trainees and FY2s should not refuse to review any babies if asked by the midwifery team. Equally, the NICU SHOs should not leave all the baby checks to their General Paediatric colleagues. The aim is for all babies to be seen in the morning and have a baby check. You should start with the babies that are likely to be discharged home the same day, but all babies on JBW should receive a baby check allowing the MWs to discharge the babies and mothers as soon as possible. Please dont leave any checks for out of hours or the next day. You will be asked to read about the routine examination of the newborn and be able to differentiate between normal variants and abnormalities that require intervention. You will have an induction on baby checks and a senior SHO or a Registrar will supervise you on your first working day (you will be observed for 10 baby checks or less if you feel confident or had previous experience). You are required at the end of the day to sign an educational agreement and you will be formally assessed with a CEX on the routine examination of the newborn. Aim to perform 3-4 checks per hour and time yourself to know your pace and be able to identify early if you need extra help. This may be difficult in the beginning and the NICU SHOs and SpRs will help you, until you acquire the skills to perform the newborn examination, learn the different management protocols and be able to manage your workload. Bleeps 5240Baby Check SHO bleep GP trainees and FY2s form the Paediatric department5495Neonatal Reviews SHO bleep NICU SHOs5496SCU SHO bleep NICU SHOs5960PN Ward SpR The Baby Check SHO bleep must be handed over in the morning by the night NICU SHO. The Baby check SHO should be informed of any babies that warrant an urgent review. At the end of the shift the baby check SHO should come up on the unit and hand over the bleep and any problems to the long day SHO. The rest of the bleeps will be kept in the doctors office on NICU out of hours. The timetable for the baby check SHOs is: Monday: 08:30 16:30 Tuesday: 08:00 16:00 Wednesday: 09:00 17:00 Thursday: 08:00 16:00 Friday: 08:00 16:00 Saturday: 08:00 11:00 Sunday: 08:00 11:00 The timetable for the SCU SHOs is: Monday: 09:00 16:00 Tuesday: 09:00 16:00 Wednesday: 09:00 16:00 Thursday: 09:00 16:00 Friday: 09:00 16:00 Saturday: 09:00 18:00 Sunday: 09:00 18:00 The PN ward SpR is expected to attend the PN ward around midday. He/She will review the babies on SCU and any babies on JBW that the SHOs have identified with abnormalities or have any questions about their examination. If this does not happen the SHOs should take the initiative and contact the SpR on their bleep. SHOs should not feel intimidated and are always welcome to discuss their queries with the SpRs or the attending Consultants. The Neonatal Unit is almost always busy but time will be made to review babies on the postnatal ward. The baby checks should be performed in the Nursery. All the equipment should be made available to you and a Nursery Nurse or a Health Care Assistant should be helping you, by gathering the babies and mothers next door with their notes. When both the Baby check SHO and the Neonatal reviews SHO are available for baby checks, the checks should still be performed in the nursery, but at no point should two families be in the same room discussing potentially sensitive data. Please try to co-ordinate between you, so that while one is taking a family history and examines a baby, the other person is filling in paperwork, prepares for blood tests or BCGs, in order to improve efficiency. Remember to check when you start in the morning whether any of the babies on your list have been antenatally identified as High Risk and are logged on the High Risk Folder (the yellow folder). A management plan (e.g. for talipes, antenatal hydronephrosis, Hepatitis B) is noted next to the babys name and problem list to help you arrange investigations and follow up. Please tick the babys name off and document the management you have carried out on the same page. This can be fed back to the Obstetric team at the mother and baby meeting on alternate Fridays during the NICU grand round. If you have any concerns or queries, please discuss them with the SpR or attending Consultant. A set of notes needs to be made up for all the babies that require anything more than a routine baby check (ie investigations, senior review, follow up). You are expected to write your examination and management plan in them so that this can be followed up if required. ***Do not write in the postnatal baby notes (blue set of notes) as the mothers take these notes home and are filled later on with the maternal notes.*** Follow up in Paediatric Outpatient Clinic The follow up appointment is booked via the secretaries in the Paediatric Outpatient Department. Please ask the JBW clerk to call 2509 or 2545 to arrange the appointment and let the secretaries know the name of the attending Consultant on NICU in order to book the appointment. If there isn't a ward clerk available a nurse or MW will need to arrange this. Family History The family history relevant to the routine examination of the newborn is poorly and inconsistently obtained. Thus, you are now asked to fill in the Red Book the section regarding the family history, on page 6. It consists of 9 questions that are answered with a yes and no format. These include: Childhood deafness; depending on the history (ie first degree relative with sensorineural deafness) you may need to discuss with a Registrar or a Consultant and arrange follow up in clinic. The HV will be performing a hearing screen on all babies in the community. Fits in childhood; The risk for unprovoked seizures is higher in children of parents who developed epilepsy before 20 years of age (nine per cent). Please advise to look out for seizures. Eye problems; Congenital cataracts and Retinoblastoma are the main concerns and require follow up (see guideline below). Hip problems; increased likelihood of DDH on first degree relatives (see guideline below). Remember to ask whether the baby was in breech position at any point in the 3rd trimester. Reading and spelling difficulties; Asthma, eczema, hay fever, allergies; increased likelihood for first degree relatives Tuberculosis; offer the BCG vaccine Heart Conditions; the incidence of congenital heart disease is around 1% and there is increased likelihood of congenital heart disease in first degree relatives. Check that the antenatal scans were normal and check whether an antenatal ECHO was performed. Look at the high risk folder in case an antenatal plan was formed. Perform a thorough cardiovascular examination and check oxygen saturations. Any other particular illnesses or conditions in the mothers or fathers family that you feel are important? BCGs The BCGs should all be performed in the morning and you can open the vial and use it for 4hrs (once reconstituted and kept in room temperature). The babies requiring a BCG should be identified antenatally and there is a section in the maternal notes indicating whether the baby needs a BCG. Please consent the parents before you perform the baby check and administer the vaccination while the baby is undressed at the end of your examination. Try to open one vial per day if possible and vaccinate as many babies as possible. If there are any extra babies for BCG vaccination in the afternoon or out of hours, then it is preferable to open another vial rather than bringing the baby back in just for the vaccination. You will be expected to observe how a BCG is given for a couple of times before you attempt to give one. A Senior SHO or a Registrar will supervise you for the first few injections until you feel confident with the procedure. This should be arranged on the same day that you are supervised for your baby check training. A DOPS form will be filled in to ensure you are competent. For the BCG guideline please click here. Special Care Unit The SCU is managed by a NICU SHO; and the SpR allocated to the PN ward should help and supervise you as required. It is helpful to have the SCU nurse with you on the ward round, so you both know the plans for the babies. There are strict criteria for SCU eligibility if you wish to admit a baby to SCU please speak to the nurse in charge. If a baby is to be discharged ensure they have: A completed formal baby check (documented in Red Book and Evolution Page) Information on the BCG vaccine and been offered it (duty of SCU SHO to consent and administer SCU babies BCG vaccine) A completed SEND discharge summary Any necessary follow-up You are also responsible for completing the SEND daily updates for the babies in SCU. SCU Ward Attendees Babies who have gone home and are coming back to the SCU for review or investigations (e.g. TFTs, prolonged jaundice screens, FBC) are booked in the SCU diary. The appointments are on Monday, Tuesday, Thursday and Friday at 14:00 & 14:30 (2 appointments available per day). These are to be used once or maximum twice for the same patient. If further follow up is required, this needs to be arranged through the Outpatient Department, with their Named Consultant (ie the Neonatal Consultant attending NICU on the day the baby was born). Their results should be reviewed daily and the appropriate action taken. This includes calling the parents to inform them of normal results or making appointments for review or further tests. The routine examination of the newborn Equipment: stethoscope, ophthalmoscope, tape measure +/- Sats probe Wash hands thoroughly (dont use alcohol gel as when you check for the sucking reflex it is bitter for the baby). Wear gloves if you prefer (youll need to handle the nappy area even if the baby has had their bowels open!). Initial Details Thoroughly review the maternal notes, regarding: antenatal scans (e.g. hydronephrosis see guideline) blood tests (e.g. Hep B / HIV see guideline) full history past medical (e.g. maternal hyperthyroidism f/u bloods required) and obstetric history pregnancy complications details of labour and delivery (ROM, type of delivery, meconium, GBS carrier, Apgars, weight) gestational age and sex of the baby There may be plans in place for postnatal investigations and management remember to check the (yellow) high risk folder. Getting started Introduce yourself Ask mother if she has any concerns about the baby. Any problems in the pregnancy Any relevant family history (e.g. hips, heart, eyes, hearing and kidneys). Fill in page 6 on the RED BOOK. Enquire about the infants progress since birth, method of feeding, adequacy of intake, alertness. Has the baby been on meconium or PROM (prolonged rupture of membrane) observations - any abnormal temperature or other observations? Has the baby had blood sugar monitoring due to hypoglycaemia risk see guideline Has the baby passed urine (most within 24hrs) and in boys is there a good stream? Has the baby passed meconium (90-95% by 48 hrs)? Was Vitamin K given i.m. or oral With oral regime TTO for follow up doses required see guideline Initial Observations - Is the infant well? Perform a general observation of the baby, including: Colour : Cyanosis, pallor, jaundice check a spun bilirubin level if concerned Blueness of hands and feet are common (acrocyanosis) Blueness of face facial petechiae common from cord around the neck / rapid second stage (facial contusion) Tip: examine the tongue it should be pink. If any doubt about possible cyanosis, check oxygen saturations. Respiratory pattern and rate should be regular and <60 breaths per minute Posture and movements baby usually active, well flexed with good tone Any dysmorphic features? Whilst baby is settled, auscultate heart: rate (normal 120-150bpm), heart sounds and murmurs Systematic approach Undress infant completely except taking off the nappy. It is best to do this gradually in stages, and examine the exposed parts of the body as you go along. Many people adopt the head to toe approach. Head Measure the head circumference if not already done by the midwife (2-3 OFC measurements, take largest) Microcephaly <32.5cm at term Head shape (symmetry), skin (bruising, lacerations), palpate anterior and posterior fontanelle, suture lines Caput- bruising and oedema of presenting part extends beyond margins of skull bones, resolves in few days Cephalhaematoma- bleeding below periostium, confined to suture lines (resolves over a few weeks) Subaponeurotic haemorrhage- collection of blood under the aponeurosis of the scalp can be accompanied by significant blood loss. Presents with shock and pallor and with a flaccid, diffuse, boggy swelling that extends across suture lines and can causing bruising behind the ears, along the posterior hair line and around the eyes. Needs urgent senior review. Ears- size, shape, position, presence of skin tags or pits Eyes- pupil size and shape, clearness of cornea and check presence of red reflex, Swollen eyelids and subconjunctival haemorrhage are not uncommon from delivery, Sticky eyes may require treatment Milia- white pimples on nose and cheeks (retention of keratin and sebaceous fluid in follicles) Mouth- tongue, palpate hard and soft palate and perform visual inspection, jaw size, look for tongue tie Neck- lumps/swellings (branchial and thyroglossal cysts, neonatal goitre- all rare) webbing/ low hairline, palpate clavicles for fractures Arms- Fractures / Erbs palsy, Hands- number of digits, finger length (clinodactly 5th finger), palmar creases, grasp reflex Chest- shape, respiratory and heart rate, heat sounds and murmurs, palpate praecordium and apex, palpate femoral pulses. Breast enlargement in either sex not uncommon (hormonal influence) Abdomen- shape, umbilical cord, palpate for liver (up to 1-2cm below costal margin is normal in neonates), spleen, kidneys and bladder Single umbilical artery- associated with renal problems in 7% cases check the findings on the anomaly scan around 22 weeks, and if the kidneys are normal and this is an isolated anomaly postnatal renal USS not indicated Genitalia Boys- testes descended?, urethral meatus normally placed?, hypospadias? Girls- hymenal tags, mucoid discharge and vagina bleeding (small amount) are common and resolve in first few weeks Tip: Urates in urine can cause salmon pinkish discharge in nappy that worries parents Anus- patency and position (anteriorly or posteriorly displaced anus may be an isolated finding or part of a syndrome). Presence of meconium does not mean anus is patent the baby can have an anorectal malformation and fistula! ALWAYS LOOK FOR A PATENT ANUS. Limbs- symmetry and movement, leg length, talipes Tone- Pull to sit (observe head control and tone) Suspend prone- observe tone and head position Spine- run finger along whole length of spine to palpate bony structures. Look for sacral dimples. Sacral dimple likely benign if small and at the gluteal crease. The base should be visible and there should be no associated redness or hairy patch. If in doubt get senior review an ultrasound is occasionally requested to look for any deeper connections. Skin Examine for rashes and birthmarks. Haemangiomas Erythema toxicum (reassure) Mongolian blue spots - base of spine and on buttocks, usually Afro-Caribbean / Asian, fade over few years, no significance but please document may be mistaken for bruising, dry skin midwives suggest olive oil or simple moisturiser. Examine primitive reflexes including Moro only if concerned about movements and posture. Hips- DDH risks- female, breech at any time in the 3rd trimester, twins with one of them lying breech, family history, oligohydramnios, talipes, lower limb abnormalities. Observe for symmetry of skin creases Perform Barlow and Ortalani examinations Barlow this examines if the hip is dislocatable. Stabilise the pelvis with one hand and with the other hand place your middle finger over the greater trochanter and the thumb around the distal medial femur. The hip is held flexed and adducted. The femoral head is gently pushed downwards /backwards. If hip dislocatable, the femoral head will be pushed posteriorly out of the acetabulum and a clunk will be palpable or audible. A click is more commonly felt and is not diagnostic of a dislocated hip. Ortalani- this examines if the hip can be returned from its dislocated position back into the acetabulum. With same grip and hip flexed and abducted, lift femoral head forwards with middle fingers (gentle upwards leverage). A dislocated hip will return with a clunk into the acetabulum. If dislocated / dislocatable hips found on examination or any risk factors present for DDH please follow the relevant protocol and refer for hip USS. Discuss examination with parents give reassurance where appropriate, and arrange any necessary follow up. If you discover an abnormality, explain the findings to the parents. If you are not able to fully satisfy them with your explanation, tell them you will speak to a senior colleague, and ask a registrar to review the baby. If you find a serious abnormality, please discuss it with a Registrar or the attending Consultant. Record examination on Evolution page and in Red book. If there are any abnormalities the baby will need to have a set of notes made up by the Joan Booker ward clerk. Do not simply record this in the maternal notes as these will not be available once the baby returns to clinic. Postnatal Ward Check Referral Forms and Contact Details Referral ProblemAppendix/AddressErbs PalsyPhysiotherapy Referral Form (Appendix A)Developmental Dysplasia of the HipOrthopaedic Referral Form (Appendix B)Congenital Talipes EquinovarusPhysiotherapy Referral Form (Appendix A)Structural TalipesPhysiotherapy Referral Form (Appendix A)Polydactyly and Skin TagsRefer to Paediatric Plastic Surgeon Miss. Catherine Milroy at St. Georges Hospital Secretary - Sharon de Coteau 020 8725 1134  HYPERLINK "mailto:sharon.decoteau@stgeorges.nhs.uk" \o "email Sharon de Coteau" sharon.decoteau@stgeorges.nhs.uk Hypospadia / ChordeeRefer to Paediatric Urologist Mr. Murphy at St. Georges Hospital Secretary Veronique Okafor 02087252290 veronique.okafor@stgeorges.nhs.ukInguinal HerniaRefer to Paediatric Surgeon Mr. Okoye at St. Georges Hospital (will be seen in clinic here) Secretary Veronique Okafor 02087252290 veronique.okafor@stgeorges.nhs.ukAbsent Red Reflex & RetinoblastomaRefer to Mr. Kafil-Hussain at SPH Fax referral letter (marked urgent) to 01784884350Hepatitis B ImmunisationReferral Letter to GP & Letter for parents - Appendix CDowns Syndrome (&other) Genetic TestingReferral Forms Appendix D Appendix A PHYSIOTHERAPY REFERRALAshford Hospital Tel: 01784 884484 Fax: 01784 884707 St. Peters Hospital Tel: 01932 722547 Fax: 01932 722635PATIENTS DETAILS: Please complete IN CAPITALSHOSPITAL NO:NHS NUMBER:DOB:SEX: Ethnicity: See below /overleafM ( F (PATIENTS SURNAME:PATIENTS FULL ADDRESS: POSTCODE:PATIENTS FORENAME:Home Tel:Mobile:INTERPRETER REQD? If Yes, which Language?  Yes ( No (Work Tel:TIME SINCE ONSET: Specify exact duration::Less than 2 weeks ( 2-6 weeks ( > 6 weeks (Transport Required? Yes ( No (OTHER (OFF WORK DUE TO CURRENT PROBLEM?  Yes ( No (DISTURBED SLEEP DUE TO THIS PROBLEM? Yes ( No (OCCUPATION FLARE UP OF CHRONIC CONDITION? Yes ( No (DIAGNOSIS / OPERATION DATE AND DETAILS: SCAN / X-RAY FINDINGS: REASON FOR REFERRAL: OTHER RELEVANT INFORMATION: REFERRERS SIGNATURE: REFERRER PRINT NAME:DATE:GP/Consultant DETAILS: Please complete IN CAPITALSGP/Consultant Name: (PRINT) Surgery Address / Stamp: (PRINT)FOR THERAPY OFFICE USE ONLY: Date ReceivedReferral source (code)Date prioritisedPriorityPrioritised by (initials)Tele contact dateLetter sent date1st Appointment or 1hr PhysioComments/Further Action: Ethnic Group Prompt Card To help us make sure that the services we provide are equally accessible and meet the needs of our diverse population we would like to have an accurate picture of the local people we serve. Please help us by giving the following information which will be treated confidentially. Indicate the ethnic group to which you feel you belong. If you are descended from more than one ethnic group please indicate the group to which you consider you most belong. O Any Other Ethnic Group OA Any Other Asian Background OW Any Other White Background P Pakistani UK White British Thank you Appendix B Please fax and then place in internal post addressed to: Rowley Bristow Orthopaedic Unit Fax number: 01932 722 689 REFERRAL TO ORTHOPAEDIC TEAM FOR DETECTION OF DEVELOPMENTAL DYSPLASIA OF THE HIP Name of baby: D.O.B: Hospital number: Address: Telephone number: Consultant: G.P. Reason for referral: Dislocated / dislocatable hip on examination (Please note these will be seen as a priority) % Clicky Hips on examination % Babies with a Family history of DDH % Breech deliveries % (Breech presentation in third trimester regardless of presentation at delivery) Both Twin Siblings % (Please refer both twins even if one twin was breech presentation or has abnormal hip examination with two separate forms) Talipes (structural/fixed) % Muscle Weakness/ other deformity % Please provide details of examination below Referring doctor (Please print): & & & & & . Signature . Date of referral . Please provide parents with  HYPERLINK "http://trustnet/docsdata/paed/DDH.doc" \o "information leaflet" information leaflet and telephone number of the Rowley Bristow Orthopaedic Outpatient appointment line (01932 722 730) Appendix C Hepatitis B Immunisation  Babys name: Babys D.O.B: Hospital number: Mothers addressograph: Date:____________ Consultant Paediatrician:_______________ Dear Doctor__________________ This patient is on the Hepatitis B Immunisation Programme. Further doses of Hepatitis B vaccine are required to complete the course, and we would be grateful if this could be arranged through your practice The next two at 1 and 2 months of age A booster at 1 year of age and pre-school booster at 5 years  Subsequent arrangements A reminder will be sent out to you and the parents at 12 months indicating that a booster is due. They will also be sent a form to have blood tests at 13 months to identify babies who have acquired hepatitis B, and to assess if there has been an adequate antibody response. The baby will be reviewed in our Outpatient Department at 14 months to discuss the results. Further doses of vaccination may be necessary. The Hepatitis B vaccine does not interfere with any of the other immunisations in the infant schedule, and they can be given as normal. Please do not hesitate to contact us should there be any problems regarding the further Hepatitis B Immunisations. Yours sincerely, Dr.__________________ Copies to: Debbie Evans, Neonatal Unit Health Visitor Dr Margot Nicholls, Consultant in Communicable Disease Control, Health Protection Unit, County Hall North, Chart Way, Horsham, West Sussex, RH12 1XA Hepatitis B Immunisation Information for Parents Babys name: Babys D.O.B: Hospital number: Mothers addressograph: Date:____________ Consultant Paediatrician_______________ Dear Parent, Your baby has received his/her first Hepatitis B vaccine. Further doses are required to complete the course, these are: The next two at 1 and 2 months of age A booster at 1 year of age and pre-school booster at 5 years These should be given by your GP practice, and a letter has been sent to them and your babys Health Visitor Subsequent arrangements You will be sent a letter at 1 year to remind you that your babys hepatitis B vaccine booster is due. You will also be sent a form to have blood tests to check the babys Hepatitis B status and their antibody levels at 13 months. Your baby will be reviewed in our Outpatient Department at 14 months to discuss the results. It may be necessary to give further doses of the vaccine. Your baby can receive all their other routine vaccines at the usual times. Yours sincerely, Dr. ____________________________ Designation _______________________ Appendix D   Commonly encountered problems: Cardiovascular system  HYPERLINK \l "HeartMurmurs"Heart murmurs  HYPERLINK \l "Cyanosis"Cyanosis Respiratory system  HYPERLINK \l "RespiratoryDistress"Respiratory Distress (Tachypnoea, Grunting, Recessions, Stridor) Neurological system  HYPERLINK \l "Jitteriness"Jitteriness vs Seizures  HYPERLINK \l "FacialNerve"Facial Nerve Palsy  HYPERLINK \l "Erbs"Erbs Palsy Gastrointestinal system  HYPERLINK \l "Vomiting"Vomiting & Bile stained vomiting  HYPERLINK \l "analatresia"Anal atresia (Imperforate Anus) & Anteriorly displaced anus  HYPERLINK \l "UmbilicalHernia"Umbilical hernia Musculoskeletal system / Orthopaedics  HYPERLINK \l "DDH"DDH  HYPERLINK \l "CongenitalTalipes"Congenital talipes equinovarus (or club foot) & talipes calcaneovalgus  HYPERLINK \l "Polydactyly"Polydactyly (& Skin Tags)  HYPERLINK \l "Syndactyly"Syndactyly  HYPERLINK \l "SacralDimple"Sacral dimple Renal system  HYPERLINK \l "Hydronephrosis"Hydronephrosis Genitalia  HYPERLINK \l "Ambiguousgenitalia"Ambiguous genitalia  HYPERLINK \l "Undescentedtestes"Undescented testes  HYPERLINK \l "Hypospadias"Hypospadias / Chordee / Buried penis / Webbed penis  HYPERLINK \l "Hydrocele"Hydrocele vs Inguinal Hernias Eyes  HYPERLINK \l "Absentred"Absent Red Reflex &  HYPERLINK \l "Absentred"Retinoblastoma Infections / BCG and other vaccinations  HYPERLINK \l "RFInfection"Risk factors for infection / GBS  HYPERLINK \l "bcgvac"BCG vaccination  HYPERLINK \l "HepB"HepB vaccination  HYPERLINK \l "HepC"Neonatal management of babies born to HepC positive mothers Feeding / Palate  HYPERLINK \l "Tonguetie"Tongue tie  HYPERLINK \l "Cleftlip"Cleft lip and/or palate  HYPERLINK \l "Weightloss"Weight loss  HYPERLINK \l "Physiotherapy"Physiotherapy F/U  HYPERLINK \l "audio"Audiology Syndromes  HYPERLINK \l "Downs"Downs Syndrome Others  HYPERLINK \l "Jaundice"Jaundice  HYPERLINK \l "Hypoglycaemia"Hypoglycaemia  HYPERLINK \l "VitK"Vitamin K administration  HYPERLINK \l "Periauricular"Peri-auricular skin tags Cardiovascular system Heart murmurs Heart murmurs affect 0.5 1% of all newborns. 46% - 62% are likely to have a benign murmur, commonly, a PDA or peripheral pulmonary artery stenosis. Perform a full cardiovascular examination and lower-limb saturation A) If the murmur is clinically soft, localised with normal pulses and saturations >95% and the baby is asymptomatic: re-examine in 24 hours time, ideally by the same person. If murmur still present, examination by a senior colleague to confirm that the murmur is clinically insignificant. If so, arrange an appointment in 4 to 8 weeks time, provide a parent information sheet on heart murmurs & advise to return to hospital if there is: Central cyanosis Respiratory distress and/or excessive sweating Poor feeding (>2 consecutive feeds of <50% usual volume) or poor weight gain B) If there is any doubt about the clinical significance of the murmur: Any potentially-significant murmurs must be reviewed by a senior colleague. Perform: CXR ECG 4-limb blood pressures Pre- and Post- ductal saturations Discuss early echocardiography with the consultant C) If limb saturations <95% and/or baby is symptomatic: See Cyanosis +/- Respiratory Distress The full guideline can be  HYPERLINK "http://trustnet/docsdata/paed/Guidelines_Neonatal/Cardiac%20Disease%20and%20Murmurs%20in%20the%20Newborn.doc" found here (Congenital Heart Disease and Neonatal Murmurs) Cardiovascular system Cyanosis Congenital heart disease (CHD) is one of the commonest congenital malformations, affecting 7 to 8 per 1000 live births The common ways in which CHD presents are: cyanosis respiratory distress a murmur cardiovascular collapse feeding difficulties or a combination of the above. Cyanosis (+/- respiratory distress) Causes include: CHD Respiratory disease Sepsis Persistent pulmonary hypertension of the newborn Methaemoglobinaemia (rare) All babies with cyanosis in the postnatal ward MUST be admitted to the neonatal unit for further investigation. Contact the on call Registrar as an emergency. The full guideline can be  HYPERLINK "http://trustnet/docsdata/paed/Guidelines_Neonatal/Cardiac%20Disease%20and%20Murmurs%20in%20the%20Newborn.doc" found here (Congenital Heart Disease and Neonatal Murmurs) Respiratory system Respiratory Distress (Tachypnoea, Grunting, Recessions, Stridor) Differential Diagnosis for a term neonate: Transient tachypnoea of the newborn Meconium aspiration Hyaline membrane disease (Surfactant deficiency) Cardiac (anatomical or persistent foetal circulation) Infection (e.g. pneumonia, septicaemia, particularly group B beta haemolytic streptococcal infection) Pneumothorax / pneumomediastinum Congenital abnormalities (e.g. tracheo-oesophageal fistula, diaphragmatic hernia, choanal atresia, hypoplastic lungs) If a baby has any signs of respiratory distress: Perform a full examination, including a detailed respiratory and cardiovascular examination Check a lower-limb saturation (if there is cyanosis urgent admission to NICU is required) Review the antenatal and perinatal Hx Consider the risk factors for infection and start antibiotics as indicated Take a CXR Check a capillary or venous blood gas Ask for regular observations on the baby / Admit to SCU Inform your seniors Neurological system Jitteriness vs Seizures The full guideline can be  HYPERLINK "http://trustnet/docsdata/paed/Guidelines_Neonatal/Encephalopathy%20and%20Seizure%20in%20the%20Newborn.doc" found here (Encephalopathy and Seizure in the Newborn Hypoglycaemia) Neurological system Facial Nerve Palsy Occurs secondary to pressure applied on the facial nerve just in front of the ear by forceps. Causes affected side of face to droop (loss of nasolabial fold, loss of angle of mouth). The infant is unable to close the eye as tight on the affected side and when the baby cries the mouth is pulled across to the normal side. In majority of cases full resolution is seen within the first weeks of life. Can cause transient feeding difficulties and if eye closure is impaired artificial tears may be required until recovery occurs. Arrange outpatient review in 6 to 8 weeks. Neurological system Erbs Palsy Brachial Plexus Injury is caused by traction to the head and neck during difficult delivery. Erbs palsy (C5, 6 nerve roots) presents with affected arm adducted and internally rotated with the elbow extended, the forearm is pronated and the wrist flexed (waiters tip position). The biceps jerk is absent and the Moro reflex is asymmetric, grasp reflex intact. May have associated fractured clavicle / humerus. 70% make a good recovery, usually begins at 2 weeks (but may take many weeks). A small number require surgical management. Plan: Ask for a review by a registrar if you are uncertain of the diagnosis. Refer the baby to physiotherapy: The babys details and contact number must be entered into the Physiotherapy day book in the office and a Physiotherapy referral form must be filled in , the Paediatric Physiotherapists can be contacted on bleep 5157. Parents will be contacted by phone / letter within 48 hours to be offered a Physiotherapy Outpatient appointment. Passive stretches taught by a Physiotherapist should begin after 48 hours to prevent joint contractures. Follow-up treatment by the Paediatric Physiotherapist is to monitor recovery and promote normal neurodevelopmental milestones. Referral will be made to a Specialist Centre if there is limited functional recovery and further treatment may be necessary. The Royal National Orthopaedic Hospital, Stanmore has a Peripheral Nerve Injury Unit, however they will not see these babies before 8-12 weeks. Babies will also have an X-ray of the arm and shoulder when seen by the Physiotherapists. If you are concerned and would like to perform an X-ray please write your finding on the referral letter to the Physiotherapists. Babies will be offered a Paediatric Doctor follow-up appointment for 6-8 weeks if recovery is minimal as they may need a follow-up appointment at a Specialist Centre to be arranged by the Physiotherapists. Gastrointestinal system Vomiting & Bile stained vomiting Worry if vomiting is: Persistent Projectile Large volume Bilious (always abnormal) Obtain from the History: History of polyhydramnios Type of delivery (SVD vs C/S) Frequency, amount and nature of vomit (ask to see clothes / blankets) Passage of meconium Abdominal distension Causes: Oesophageal atresia - polyhydramnios, unable to swallow saliva, feeding causes vomiting, coughing, choking and cyanosis Duodenal atresia and Malrotation - bilious vomiting Distal Intestinal Obstruction- vomiting sometimes bilious, distended abdomen, failure to pass meconium; Hirchsprungs disease, meconium ileus, ileal and colonic atresia Anorectal malformation Sepsis (including UTI) Inborn errors of metabolism Gastro-oesophageal Reflux Cow's milk protein intolerance Pyloric stenosis (doesnt usually present in the first 2 weeks of life) Investigations: Abdominal X-ray U&Es CRP Blood gas (with lactate) Blood sugar level Management: Bilious vomiting is always abnormal Discuss with seniors urgently If there are concerns regarding sepsis start antibiotics Admit to SCU / Inform SpR Gastrointestinal system Anal atresia (Imperforate Anus) & Anteriorly displaced anus / Anorectal Malformations Anorectal Malformations / Imperforate anus are associated with an increased incidence of some other specific anomalies as well, together being called the VACTERL association: V - Vertebral anomalies A - Anal atresia C - Cardiovascular anomalies T - Tracheoesophageal fistula E - Esophageal atresia R - Renal (Kidney) and/or radial anomalies L - Limb defects Management plan: Inform your seniors urgently Keep the baby nil by mouth and start iv Dextrose 10% Pass a large bore NGT Try to exclude any obvious associated abnormalities as mentioned above Transfer to a surgical centre is required Anteriorly displaced anus Anterior ectopic anus is different from imperforate anus with perineal fistula in that the anal opening is usually of normal size, and only mildly misplaced. Most of these children develop severe constipation. Surgery to relocate the anterior anus is simple, but does not change the fact that these children often have life-long problems with constipation independent of the actual anal location. Management plan: You need to exclude any other associated abnormalities (VATER / VACTREL association) Referral to the Paediatric Surgeons should be discussed with the SpR or Consultant References: Paediatric Surgeons of Phoenix Surgeons website:  HYPERLINK "http://www.surgery4children.com/index.php?option=com_content&view=article&id=145:anterior-ectopic-anus&catid=51:abdomen&Itemid=142"http://www.surgery4children.com/index.php?option=com_content&view=article&id=145:anterior-ectopic-anus&catid=51:abdomen&Itemid=142 University Hospital of Southampton NHS Foundation Trust website:  HYPERLINK "http://www.uhs.nhs.uk/OurServices/Childhealth/Neonatalsurgery/Conditionswetreat/AnorectalMalformations.aspx"http://www.uhs.nhs.uk/OurServices/Childhealth/Neonatalsurgery/Conditionswetreat/AnorectalMalformations.aspx Gastrointestinal system Umbilical Hernia Common especially in babies of African origin. Results from failure of umbilical ring to obliterate. Can be large, reducible and do not cause symptoms (warn parents hernia enlarges when baby cries / strains due to increased intra- abdominal pressure and it is not the hernia which is causing the crying / straining). Majority resolve over first few years of life. No referral required. GP to refer to surgeons if not resolved by 4 years. Musculoskeletal system / Orthopaedics DDH The incidence is about 0.3% and is three times more common in girls. Management plan: Refer for to the Rowley Bristow Orthopaedic Clinic all babies with: An abnormal hip examination including clicky, dislocatable and dislocated hips (pls ask for a senior review if uncertain) A family history of Hip Dysplasia (first degree) Breech deliveries (third trimester presentation regardless of presentation at delivery) Both twin siblings (refer both twins even if only one baby delivered by breech presentation or has abnormal hip examination) Talipes (structural/ fixed) Muscle weakness or other deformity The DDH Referral Form to the Rowley Bristow Orthopaedic Clinic can be  HYPERLINK "http://trustnet/docsdata/paed/Guidelines_Neonatal/Developmental%20Dysplasia%20of%20the%20Hips%20-%20Referral%20Form.doc" found here please fax the form to: 01932 872 015 and also post referral by internal mail within 24 hours of detection. Give parents DDH Information Leaflet ( HYPERLINK "http://trustnet/documents/leaflets/new/DDH.pdf" click here) and advise them to phone Appointments (01932 722 730) in the Rowley Bristow Orthopaedic Unit in two weeks if they have not received an appointment. The paediatric team DO NOT have to arrange ultrasound scans. All referrals for abnormal hip examination will be urgently reviewed and a hip ultrasound will be performed. For all other referrals, e.g. high risk cases, an ultrasound scan will be performed between three and six weeks. The full guideline can be  HYPERLINK "http://trustnet/docsdata/paed/Guidelines_Neonatal/Developmental%20Dysplasia%20of%20the%20Hip.doc" found here (DDH Guideline) Musculoskeletal system / Orthopaedics Congenital talipes equinovarus (or club foot) & talipes calcaneovalgus In talipes equinovarus, the heel is turned inwards and the whole foot is rolled inwards with the toes pointing upwards. It is a common birth defect, occurring in about one in every 1,000 live births. Approximately 50% of cases of clubfoot are bilateral. This occurs in males more often than in females by a ratio of 2:1. Can be positional or structural.  HYPERLINK "http://upload.wikimedia.org/wikipedia/commons/2/28/P3240003.jpg" Picture of a baby with talipes equinovarus (source: Wikipedia  HYPERLINK "http://en.wikipedia.org/wiki/Club_foot"http://en.wikipedia.org/wiki/Club_foot) In talipes calcaneovalgus, the foot is turned outwards with the toes pointing upwards (mainly positional) Positional Talipes The foot is of normal size, the deformity is mild and the foot can easily be manipulated into the normal position. Management plan: Provide parents with the Personal Exercise Program leaflet Refer to the physiotherapists: Babies details and contact number must be written in the Physiotherapy Day book in the office and a Physiotherapy referral form filled in. Cover is available up to 5 pm by the Paediatric physiotherapists, who can be contacted on bleep 5157. Parents will be contacted by phone or letter within 24 hours to arrange follow-up by the Paediatric Physiotherapists. Structural Talipes In structural talipes equinovarus, the affected foot is shorter and the calf muscles are thinner than normal. The position of the foot is fixed and can't be easily corrected. Management plan: Refer to the physiotherapists as urgent - serial casting is required: Any baby with a structural talipes will commence Ponsetti management as early as appropriate (although preterm babies need to be 38 weeks gestation). Serial casting weekly (on average x6 casts) until correction is satisfactory. A purcutaneous tenotomy is required in at least 80% of cases at the end of casting. When the correction is complete, the babies feet are splinted in boots and bar for x3 months full time and during sleep up to the age of 4 years. In a small number of cases further treatment of casting or other operations may be required. Post tenotomy the baby will have a review appointment with the Consultant when standing at about 1 year of age. There will be Annual reviews with the Consultant up to 5 years . Referral for possible DDH: Any baby who has needed on-going treatment will be given an appointment in the Childrens Orthopaedic Clinic within 6 -8weeks to have a hip U/S Scan to be arranged by the Physiotherapists. Musculoskeletal system / Orthopaedics Polydactyly (& Skin Tags) Define extra digits as pre-axial (radial side of hand, medial side of toes) - higher association with other anomalies axial (midline) post-axial (ulnar side of hand, lateral side of toes) - often have strong family history Do not tie off skin tags or extra digits with silk as this often leaves unsightly tags. Refer to plastic surgery - Miss Catherine Milroy, Consultant Plastic Surgeon at St Georges Hospital All patients with accessory digits or skin tags are to be referred to the plastic surgery service at the time of discharge from the postnatal ward. Please do not ask them to wait until they have been seen by the GP or in clinic to be referred. Pedunculated accessory digits can be managed using a ligaclip device. It is said to be most effective when done early at less than 6 weeks of age. Miss Milroy will however still use this technique in babies up to the age of 3 months. It is a quick, straightforward procedure that is done without local or general anaesthesia and the babies settle down quickly once they have had a feed post procedure. After 3 months of age, the management will include a general anaesthetic, so it is vital these babies are referred early. Contact Number for Miss Catherine Milroy s secretary: 02087251134 / Fax N: 02087252416 Musculoskeletal system / Orthopaedics Syndactyly Syndactyly is a condition wherein two or more digits are fused together. Can be simple or complex: In simple syndactyly, adjacent fingers or toes are joined by soft tissue. In complex syndactyly, the bones of adjacent digits are fused. Can be complete or incomplete: In complete syndactyly, the skin is joined all the way to the tip of the finger In incomplete syndactyly, the skin is only joined part of the distance to the fingertip. Syndactyly can be an isolated finding, or it can be found in association other abnormalities ( eg Poland syndrome, Apert syndrome or Holt-Oram syndrome). Syndactyly of the border digits (thumb/ index finger or ring/ small fingers) is treated at early age to prevent the larger digit from curving towards the smaller digit with growth. Typically, syndactyly of these digits is treated at 6 months of age. The treatment of syndactyly of the other digits is elective and is more commonly performed when the digits have grown, at 18 24 months of age. Management plan: Perform a detailed examination and look out for associated abnormalities Inform your seniors Consider X-rays of the affected limbs Refer the baby to Plastic Surgeons for simple syndactyly (ie no bony involvement) and Orthopaedics for complex syndactyly (ie underlying bone deformity) - please discuss with the SpR or Consultant on call. Arrange for follow up in clinic with the attending consultant in 6-8 weeks if syndactyly is not an isolated finding Musculoskeletal system / Orthopaedics Sacral Dimple If a sacral dimple is noted during the baby check, please ensure you can see the base and that there is no sinus to the skin. If the dimple is at the tip of the coccyx, the baby has a normal lower-limb neurological examination and there are no skin marks or extra hair over the spine, then you can reassure parents and no action is required. If the dimple is over the lumbar area, you can't see the base and there are extra hair or rashes, please inform your SpR and arrange for an USS of the lower spine. Renal system Hydronephrosis Measurement of the maximum anteroposterior diameter of the renal pelvis (RPD): Anomaly scan at 22 weeks RPD of > 5mm is considered to be abnormal. Mild cases with will have a repeat scan at 34 weeks at St. Peters Hospital. More severe cases may be scanned more frequently, or referred to St.Georges Hospital for further management. At 34 weeks AP diameter < 6mm is normal and no further intervention is required. AP diameter >10 mm is abnormal and should be further investigated. AP diameter 6 9 mm is a grey area, and management is highly controversial. Currently our ultrasonographers may report this group as normal, or report the actual diameter. Postnatal Our radiologists consider RPD > 7mm to be abnormal (if USS performed after 48 hours and before 6 weeks). After 6 weeks postnatal age >10mm is considered to be abnormal. Management plan: Perform a physical examination to detect the presence of an abdominal mass (possible PUJ or MCDK) or palpable bladder (PUV). RPD 6 - 9mm at 34 week scan or RPD 10 - 15 mm at 34 week scan Start prophylactic antibiotics Trimethoprim 2mg/kg once daily. Please fill out a hospital TTO form, or if an FP10 is used out of hours, please clearly document in the babys notes the dose of Trimethoprim prescribed. Ultrasound scan (USS) of kidneys at 4 - 6 weeks Arrange outpatient appointment for 6 8 weeks; ideally indicate on USS request form when the date of the OPA is, as the radiology department will then ensure the USS is carried out prior to the clinic appointment. RPD >15mm at 34 weeks Start prophylactic antibiotics Trimethoprim 2mg/kg once daily. Please fill out a hospital TTO form, or if an FP10 is used out of hours, please clearly document in the babys notes the dose of Trimethoprim prescribed. Request early USS (ideally at 72 hours). Suspect bladder outlet obstruction if bilateral in a male. This requires urgent investigation with USS and MCUG to exclude posterior urethral valves - see management of bladder outlet obstruction. If the mother has been seen at a tertiary centre, a clear plan should be outlined in her notes and should be followed accordingly. The full guideline can be  HYPERLINK "http://trustnet/docsdata/paed/Guidelines_Neonatal/Renal%20Uropathies.doc" found here (Renal Uropathies) under review Other renal uropathies The full guideline can be  HYPERLINK "http://trustnet/docsdata/paed/Guidelines_Neonatal/Renal%20Uropathies.doc" found here (Renal Uropathies) Genitalia Ambiguous genitalia If there is uncertainty over the sex of a baby review the baby as a matter of urgency. Underlying causes include Congenital Adrenal Hyperplasia which may cause salt loosing crisis. Initial Management: Contact the Registrar and Consultant urgently. Check U&Es and a Blood Sugar Level urgently Do not designate a gender Further Management: Chromosomes need to be checked after obtaining parental written consent Check urinary and blood steroid profile Arrange for an USS of the pelvis (to establish whether the baby has a uterus) * Remember not to designate a gender until the baby is fully investigated* Genitalia Undescented testes (Cryptorchidism) 3% male term infants vs 33% male premature infants Majority descend in the first few months after birth. If remain undescended beyond first few years of life increased incidence of testicular cancer (x20), and infertility (sperm count reduced if testes in abdomen). Management plan: Unilateral Undescended Testes: Refer to GP to review at 6 weeks; they will refer to surgeons if testes remain undescended at that point. Bilateral Undescented Testes: Discuss with the Registrar, as this raises the possibility of a virilised female infant see ambiguous genitalia above. An abdominal USS may be required to visualise the testes and confirm absence of a uterus. Genitalia Hypospadias / Chordee / Buried penis / Webbed penis Referral to Paediatric Urologists may be required for hypospadius and chordee. Discuss with the Registrar regarding need for referral. Advise the family not to have the baby circumcised, at least until the baby is seen by the Urologists. Genitalia Hydrocele vs Inguinal Hernias Hydrocele: Accumulation of fluid in tunica vaginalis due to persistence of a narrow patent processus vaginalis. Typically scrotal, can be large, smooth and non tender. Transilluminates and is not reducible. Majority resolve in first 6-12 months (obliteration of patent processus vaginalis continues after birth) and so no initial surgical follow up indicated. If persist beyond a year GP should refer to surgeons. Inguinal Hernia: 1-2% term newborns - 90% males Increased incidence in preterm babies (20-30% premature males). Majority direct (1% indirect) Right > Left - 5%-10% are bilateral Present as intermittent swelling in the groin or scrotum especially on crying or straining. Refer to Paediatric surgeons for operative repair at diagnosis. Risk of incarceration: baby presents as unwell (crying, irritable), vomiting, abdominal distension, mass becomes red, tender and irreducible. Eyes Absent Red Reflex & Retinoblastoma The red reflex test is used to screen for abnormalities of the back of the eye (posterior segment) and opacities in the visual axis, such as a cataract or corneal opacity. An ophthalmoscope held close to the examiners eye and focused on the pupil is used to view the eyes from 12 to 18 inches away from the subjects eyes. To be considered normal, the red reflex of the 2 eyes should be symmetrical. Dark spots in the red reflex, a blunted red reflex on 1 side, lack of a red reflex, or the presence of a white reflex (retinal reflection) are all indications for referral to an ophthalmologist. Infants or children in high-risk categories, including relatives of patients with: retinoblastoma infantile or juvenile cataracts retinal dysplasia, glaucoma other vision-threatening ocular disorders that can present in infancy should not only have red reflex testing performed in the nursery but also be referred to an ophthalmologist who is experienced in examining children for a complete eye examination regardless of the findings of the red reflex testing by the pediatrician. Management plan: All babies with an absent red reflex need to be reviewed by the Registrar and referred to the Ophthalmologists. Mr Kafil-Hussain is our local Consultant Ophthalmologist who reviews all the neonates, please address the referral to him. For the neonates in the high-risk category please arrange a follow up in clinic with Mr Hussain (please send a referral letter to Mr Hussain with the details of the patient and the reason for the request). References: Policy Statement, Red Reflex Examination in Neonates, Infants and Children, American Academy of Paediatrics, Volume 122, Number 6, December 2008 Infections / BCG and other vaccinations Risk factors for infection / GBS Risk factors for infection: Prolonged rupture of membranes GBS colonisation Maternal pyrexia peri-natally Fetal tachycardia Need for resuscitation at birth Abnormal observations on the neonate postnatally Recognition of sick infant Signs and Symptoms (often subtle): ! HR, ! RR +/- increased work of breathing Heart murmur Poor skin perfusion, skin mottling, cyanosis Quiet, not feeding well Temperature instability Lethargy, floppiness, full sunken fontanelle Abnormal movements (often focal and subtle) Irritable, high pitched cry Feed intolerance, abdominal distension Abdominal distension, enlarged liver Nursing staff or parents concerned Special Situations 1. Positive High Vaginal Swab result after mother and baby discharged home: Baby < 36 hours old: admit baby and follow the GBS protocol Baby > 36 hours old: baby to be assessed by doctor/ midwife by phone. If necessary a hospital assessment will be arranged. 2. Mothers who wish to go home before 24 hours of observation is complete SHO should discuss with middle grade doctor or consultant. Document in the notes that mother wished to go home against medical advice and ensure that the baby is followed up by community midwife within 24 hours of discharge. If antibiotics have been given, once they are stopped the baby does not need 24 hours observation and can go home straightaway. Management plan: If a baby needs iv antibiotics please admit the baby to the SCU. Obtain iv access and send bloods off for FBC, CRP, B/C and blood gas. Start iv Co-amoxiclav (first line Abx for neonates) Admit the baby to Badger Inform seniors The full guideline for neonatal sepsis and GBS can be  HYPERLINK "http://trustnet/docsdata/paed/Guidelines_Neonatal/Group%20B%20Streptococcus%20and%20Neonatal%20Sepsis.doc" found here. Infections / BCG and other vaccinations BCG vaccination Intended Benefits: Provides protection against tuberculosis. A live attenuated vaccine derived from Mycobacterium bovis which stimulates the development of hypersensitibity to M. tuberculosis. Disadvantages / Complications: 20% failure rate of the BCG vaccination. The expected reaction to successful BCG vaccination is initially induration at site of injection. At 2 or more weeks a local lesion starts as a pustule and then may ulcerate and subsides over several weeks or months leaving a small flat scar. If the lesion becomes large (>1mm), begins to discharge or an abscess forms, medical advice should be sought. No live vaccine should be administered within 4 weeks of the BCG vaccine (none of the scheduled vaccines given within the first 12 months are live; the first live vaccination is the MMR which is given at 13 months). No vaccination should be given into the left arm for at least 3 months due to the risk of lymphaedenitis (scheduled vaccines in the first year of life are normally given into the anterolateral aspect of the thigh). Recommended for: All infants (aged 0 to 12 months) living in areas where the incidence of TB is 40/100,000 or greater. Local areas Include Hounslow, Feltham, Bedfont. All infants (aged 0 to 12 months) with a parent or grandparent who was born in a country where the incidence of TB is 40/100,000 or greater.  HYPERLINK "https://www.gov.uk/government/uploads/system/uploads/attachment_data/file/491527/WHO_estimates_of_tuberculosis_incidence_by_country__2014_v2.pdf" https://www.gov.uk/government/uploads/system/uploads/attachment_data/file/491527/WHO_estimates_of_tuberculosis_incidence_by_country__2014_v2.pdf Intention to visit/live in a high-incident country for 3 months or more. Family history of TB in the past 5 years. Prior to vaccination: Ensure that the maternal HIV status is negative. Provide the TB, BCG vaccine and your baby leaflet to the parents and talk through the intended benefits and possible complications of the vaccine. Obtain informed written consent (premade form). Documentation of the vaccination: In the RED BOOK On the postnatal case notes In the blue BCG folder Ensure you document the date, site and method of administration, batch no. and expiry date and sign. Preparing the vaccine: Obtain 1 vial of BCG vaccine and a 1ml vial of BCG solvent. Prior to mixing ensure BCG vaccine has been stored in fridge and check expiry date. Draw up 1ml of the solvent into a 2 ml syringe using green (21G) needle and inject into BCG vaccine vial. Allow BCG vial to stand for 1 minute (do not mix or shake) Once made up the vaccine should be used within 4 hours. Administration of vaccine: Using a 1ml syringe draw up required volume (neonate 0.05ml) of BCG vaccine from BCG vial. Firmly attach a short bevel 25G (orange) or 26G (brown) needle onto the end of the syringe and ensure all air is expelled and the needle hub is filled with vaccine. The BCG vaccine must be given intradermally into the left arm at the insertion of the deltoid muscle onto the humerus. Subcutaneous injections can lead to abscess formation, adenitis and other complications. Undress baby so left upper arm is easily accessible Position the baby so that left arm accessible and in extended position (ideally in parents arms or lying on a flat surface) Stretch the skin between thumb and forefinger and insert needle (25 or 26G) bevel upwards) into the superficial layer of the dermis (almost parallel with the surface, bevel can usually be seen under the skin) for about 3mm. Inject vaccine slowly, considerable resistance is felt if vaccine administered correctly. If resistance is not felt the needle is too deep and should be removed and re-inserted before giving more vaccine. 0.05ml of vaccine should give a 3mm bleb A piece of sterile cotton wool or gauze can be placed on the site of injection for a few minutes but the site should not be covered for any period of time. References: Immunisation against infectious disease - 'The Green Book'  HYPERLINK "http://www.dh.gov.uk/en/Publichealth/Healthprotection/Immunisation/Greenbook"www.dh.gov.uk/en/Publichealth/Healthprotection/Immunisation/Greenbook BNF for Children BNF 2008  HYPERLINK "http://www.bnfc.org/"www.bnfc.org Guidelines for the administration of intradermal BCG  HYPERLINK "http://www.cumbria.nhs.uk/pct/about/publications/policies/clinical/guidelines_for_Intradermal.pdf"www.cumbria.nhs.uk/pct/about/publications/policies/clinical/guidelines_for_Intradermal.pdf Infections / BCG and other vaccinations Hep B vaccination The full guideline can be found here ( HYPERLINK "http://trustnet/docsdata/paed/Guidelines_Neonatal/Hepatitis%20B%20immunisation.doc" Hepatitis B immunisation &  HYPERLINK "http://trustnet/docsdata/paed/Guidelines_Neonatal/Hepatitis%20B%201%20yr%20vaccine%20reminder.doc" Hepatitis B 1 yr vaccine reminder) Neonatal management of babies born to Hep C positive mothers The full guideline can be found here ( HYPERLINK "http://trustnet/docsdata/paed/Guidelines_Neonatal/Hepatitis%20C%20positive%20mothers%20-%20neonatal%20management.doc" Hepatitis C positive mothers - neonatal management) Feeding / Palate Tongue tie Discuss with Infant Feeding team Cleft lip and/or palate The condition is usually detected antenatally. Cleft lip and/or palate can be an isolated finding or part of a syndrome. Check baby carefully for any other congenital abnormalities. An isolated cleft palate is more easily missed, so remember to visualise the palate during the baby check. The baby may also present with milk regurgitation through the nose. If the baby is term and there are no other abnormalities, the baby can be nursed on the postnatal ward or special care unit. Breastfeeding is often possible but may need a bottle with a special teat. Cleft lip is usually repaired at around 3 months and palate between 6 and 9 months. Management plan: Perform a thorough examination of the baby and exclude any other abnormalities. If the diagnosis was made antenatally, the family will be known by South Thames Cleft Lip and Palate service (CLAPA team). Please inform the CLAPA team once the baby is delivered on 07717571931. If the condition was noted once the baby was born, please request a senior review from the Registrar and/or Consultant. Contact the CLAPA team as soon as possible. Feeding / Palate Weight loss Term babies may loose 4-7% of their weight after birth. Breast fed babies tend to loose more (5-10%) than bottle fed babies (2-6%). Term babies usually regain their birth weight in the 2nd week of life and pre-term babies in the 3rd week of life. Weight loss of > 10% of the birth weight is a cause for concern. Commonest Causes: Poor intake Breast feeding problems Other Causes: Infection Inborn errors of metabolism Malabsorption Congenital cardiac disease Take a detailed feeding history: How much milk How long is the baby feeding for How often is the baby feeding for Problems with latching on / sucking Hx of vomiting Number of wet and dirty nappies Nature of stool Hx of lethargy Presence of jaundice Management plan: Consider admission to the neonatal unit or SCU if the baby is on the postnatal ward Assess clinically for signs of dehydration, jaundice, cardiac disease Investigations: Consider U&Es, LFTs, blood gas, BSL, FBC, CRP, B/C, urine MC&S Start antibiotics if there are risk factors for infection perinatally or the baby looks clinically unwell. Treatment options: Top up feeds (bottle / cup / NGT) are preferred vs IV fluids Offer feeding advice; involve the breast feeding advisor or a midwife. Physiotherapy F/U Audiology All babies have a universal newborn hearing screen and high risk babies (eg babies with jaundice or FHx of deafness) will receive enhanced screening. Syndromes Downs Syndrome If you are suspecting the diagnosis of Down's syndrome on a newborn baby please inform the parents of the specific findings you have and record them in your notes. Do not give parents a diagnosis of Down's at this stage. Inform the Neonatal Registrar or Consultant urgently to review. If the diagnosis is still considered bloods will be required for FISH and Chromosomes please obtain written parental consent and fill in the relevant forms. A useful source of information for parents and professionals is the Down's Association Syndrome website:  HYPERLINK "http://www.downs-syndrome.org.uk/"http://www.downs-syndrome.org.uk/ Please find the full guideline  HYPERLINK "http://trustnet/docsdata/paed/Guidelines_Neonatal/Downs%20Syndrome%20Management.doc" here Others Jaundice NICE has published a guideline on the management of Neonatal Jaundice. The Quick reference guide can be found here:  HYPERLINK "http://guidance.nice.org.uk/CG98/QuickRefGuide/pdf/English"http://guidance.nice.org.uk/CG98/QuickRefGuide/pdf/English The Treatment Threshold Charts (Bilirubin Charts) can be found here:  HYPERLINK "http://www.nice.org.uk/nicemedia/live/12986/48580/48580.pdf"http://www.nice.org.uk/nicemedia/live/12986/48580/48580.pdf The full guidelines for Prolongued Jaundice screen and Management of jaundice in the community can be found here  HYPERLINK "http://trustnet/docsdata/paed/Guidelines_Neonatal/Jaundice%20-%20Community%20Management.doc" Jaundice - Community Management  HYPERLINK "http://trustnet/docsdata/paed/Guidelines_Neonatal/Jaundice%20-%20Prolonged%20Screening%20Guideline.doc" Jaundice - Prolonged, Screening Guideline Others Hypoglycaemia The full guideline can be found here  HYPERLINK "http://trustnet/docsdata/paed/Guidelines_Neonatal/Hypoglycaemia%20-%20Neonatal%20Management.doc" Hypoglycaemia: Guidelines for the Prevention and Management of Hypoglycaemia  HYPERLINK "http://trustnet/docsdata/paed/Guidelines_Neonatal/Hypoglycaemia%20-%20Prevention%20in%20the%20High%20Risk%20Infant.doc" Hypoglycaemia: Prevention of Hypoglycaemia in the High Risk Infant - Care Plan Neonatal Hypoglycaemia Others Vitamin K administration All babies should have vitamin K to prevent haemorrhagic disease of the newborn. Vitamin K deficiency bleeding is rare and can occur early (1st week) or late (week 1-8). Symptoms include: bruising, haematemesis & maleana, bleeding from umbilical stump or after circumcision, rarely intracranial haemorrhage. IM Vitamin K: Term babies should receive 1mg i.m. Vitamin K as soon as possible after birth. Preterm babies should receive Vitamin K im: 0.5mg if <1.5kg and 1mg if >1.5kg. IM vitamin K is recommended in the following situations (as the oral absorption is variable): Prematurity (<37 weeks) Unwell baby Instrumental delivery Neonatal hypoxic ischemic encephalopathy Maternal liver disease or taking enzyme inducing drugs (anticonvulsants, cepahlosporins, anti-TB drugs and warfarin) Oral Vitamin K: If parents do not wish to have the IM preparation an oral alternative is available (phytomenadione). Prescribe on the drug chart and as a TTO (via the inpatient list / 3 copies): 1st dose: 2mg - Day 0 (at birth) 2nd dose 2mg - Day 4 to 7 3rd dose: 2mg - 1 month of age if the baby is exclusively breast fed (omitted if formula fed) For further information see: BNF for Children 2008  HYPERLINK "http://www.bnfc.org/"Tvwx  # $ % C D F G f g h } ~  " # $ % E jhqxUjKhqxUjhqxUjShqxUjhqxUjohqxU hqx0JjhqxUjhqxUhqx hqx5\hqxCJ$aJ$78UVWtuvw E F  $ n " O  & Fh^h$a$E F G l m n o ! 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It is important that these babies are seen early at the specialist centre so that Miss Milroy can select the ones that can also be managed as above. Late referrals will increase the likelihood of missing out on this window and increases the chances of procedures under general anaesthesia. The anaesthetists at St Georges prefer to wait until the children are at least 10 months old for such elective plastic procedures.  Finally, please ensure that the patient details are accurate and that the named consultant is always aware and copied into any referrals. Authors: Kornilia Nikaki, Tracy Lawson, Dr. Lisa Husband, July 2012 Minor update March 2017 for BCG by Dr Khalid     Page  PAGE 49 F*H*I*J*K*L*M********!+N+O+Q+R+T+U+W+X+Z+[+m+ B#%$d Ngd9,NgdWQ$a$$a$m+n+o+p+gdWQ20p1. A!n"n#7$n% 9 00p1. A!n"n#7$n% P 5 00p1. A!n"n#7$n% 9 00p1. A!n"n#7$n% P 5 00p1. 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