Targeting protein homeostasis in sporadic inclusion body ...
tolerated. Although arimoclomol improved some IBM-like pathology in the mutan tVCPmouse,wedidnotsee statistically significant evidence of efficacy in the proof -of-concept patient trial. INTRODUCTION Sporadic inclusion body myositis (sIBM) is the commonest idiopathic inflammatory myopathy (IIM) occurring in patients more than 50 years ................
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